fig7

Figure 7. Patient #27 (14.3 and 18.8 years) with progressive ABCA4-IRD. W-OCT, central horizontal scan: (A) Disintegration of the outer retinal layers in the foveal and parafoveal region. (B) Progressed disintegration in the foveal area as well as peripheral progression of disintegration beyond the macular area (4 years later). W-OCT, superior horizontal scan tangentially to the upper temporal vascular arcade: (C) Normal structure of retinal layers. (D) Flecks of irregular outer retinal layers and SRM (4 years later).